[Term] id: PR:Q8N5Z0-2 name: kynurenine/alpha-aminoadipate aminotransferase, mitochondrial isoform h2 (human) def: "A kynurenine/alpha-aminoadipate aminotransferase, mitochondrial (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q8N5Z0-2." [PRO:DNx, UniProtKB:Q8N5Z0] comment: Category=organism-sequence. synonym: "hAADAT/iso:h2" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q8N5Z0-2 is_a: PR:Q8N5Z0 ! kynurenine/alpha-aminoadipate aminotransferase, mitochondrial (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:000046214 name: kynurenine/alpha-aminoadipate aminotransferase, mitochondrial, transit peptide removed pyridoxal phosphate lysine 1 (human) def: "A kynurenine/alpha-aminoadipate aminotransferase, mitochondrial (human) that has had the transit peptide removed and has been post-translationally modified to include pyridoxal phosphate lysine at position 263 of the amino acid sequence represented by UniProtKB:Q8N5Z0. UniProtKB:Q8N5Z0, 30-425, Lys-263, MOD:00128." [PRO:DNx, Reactome:R-HSA-70943] comment: Category=organism-modification. synonym: "hAADAT/TransPep-/Pyrdox:1" EXACT PRO-short-label [PRO:DNx] synonym: "PRO_0000020602, Lys-263, MOD:00128" EXACT PRO-proteoform-ftid [PRO:DNx] synonym: "UniProtKB:Q8N5Z0, 30-425, Lys-263, MOD:00128" EXACT PRO-proteoform-std [PRO:DNx] xref: Reactome:R-HSA-70943 "PR:000046214 located_in GO:0005759" is_a: PR:Q8N5Z0 ! kynurenine/alpha-aminoadipate aminotransferase, mitochondrial (human) relationship: has_part MOD:00128 ! N6-pyridoxal phosphate-L-lysine relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens relationship: lacks_part SO:0000725 ! transit_peptide [Term] id: PR:Q8N5Z0-1 name: kynurenine/alpha-aminoadipate aminotransferase, mitochondrial isoform h1 (human) def: "A kynurenine/alpha-aminoadipate aminotransferase, mitochondrial (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q8N5Z0-1." [PRO:DNx, UniProtKB:Q8N5Z0] comment: Category=organism-sequence. synonym: "hAADAT/iso:h1" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q8N5Z0-1 is_a: PR:Q8N5Z0 ! kynurenine/alpha-aminoadipate aminotransferase, mitochondrial (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:Q8N5Z0 name: kynurenine/alpha-aminoadipate aminotransferase, mitochondrial (human) def: "A kynurenine/alpha-aminoadipate aminotransferase, mitochondrial that is encoded in the genome of human." [PRO:DNx, UniProtKB:Q8N5Z0] comment: Category=organism-gene. synonym: "KAT2" RELATED Gene-based [UniProtKB:Q8N5Z0] synonym: "AADAT" RELATED Gene-based [UniProtKB:Q8N5Z0] synonym: "KYAT2" RELATED Gene-based [UniProtKB:Q8N5Z0] synonym: "hAADAT" EXACT PRO-short-label [PRO:DNx] synonym: "AadAT (human)" EXACT [UniProtKB:Q8N5Z0] synonym: "KAT/AadAT (human)" EXACT [UniProtKB:Q8N5Z0] synonym: "glycine transaminase AADAT (human)" EXACT [UniProtKB:Q8N5Z0] synonym: "2-aminoadipate transaminase (human)" EXACT [UniProtKB:Q8N5Z0] synonym: "kynurenine aminotransferase II (human)" EXACT [UniProtKB:Q8N5Z0] synonym: "2-aminoadipate aminotransferase (human)" EXACT [UniProtKB:Q8N5Z0] synonym: "alpha-aminoadipate aminotransferase (human)" EXACT [UniProtKB:Q8N5Z0] synonym: "kynurenine--oxoglutarate transaminase 2 (human)" EXACT [UniProtKB:Q8N5Z0] synonym: "kynurenine--oxoglutarate transaminase II (human)" EXACT [UniProtKB:Q8N5Z0] synonym: "kynurenine--glyoxylate transaminase AADAT (human)" EXACT [UniProtKB:Q8N5Z0] synonym: "methionine--glyoxylate transaminase AADAT (human)" EXACT [UniProtKB:Q8N5Z0] synonym: "kynurenine--oxoglutarate aminotransferase II (human)" EXACT [UniProtKB:Q8N5Z0] xref: UniProtKB:Q8N5Z0 intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens intersection_of: PR:000003525 ! kynurenine/alpha-aminoadipate aminotransferase, mitochondrial relationship: has_gene_template HGNC:17929 ! AADAT (human) [Term] id: PR:000003525 name: kynurenine/alpha-aminoadipate aminotransferase, mitochondrial def: "A protein that is a translation product of the human AADAT gene or a 1:1 ortholog thereof." [PRO:DNx] comment: Category=gene. synonym: "KAT2" RELATED Gene-based [] synonym: "AADAT" EXACT PRO-short-label [PRO:DNx] synonym: "AadAT" EXACT [] synonym: "KYAT2" RELATED Gene-based [] synonym: "KAT/AadAT" EXACT [] synonym: "glycine transaminase AADAT" EXACT [] synonym: "2-aminoadipate transaminase" EXACT [] synonym: "kynurenine aminotransferase II" EXACT [] synonym: "2-aminoadipate aminotransferase" EXACT [] synonym: "alpha-aminoadipate aminotransferase" EXACT [] synonym: "kynurenine--oxoglutarate transaminase 2" EXACT [] synonym: "kynurenine--oxoglutarate transaminase II" EXACT [] synonym: "kynurenine--glyoxylate transaminase AADAT" EXACT [] synonym: "methionine--glyoxylate transaminase AADAT" EXACT [] synonym: "kynurenine--oxoglutarate aminotransferase II" EXACT [] is_a: PR:000000001 ! protein