[Term] id: PR:000008549 name: 3-hydroxyisobutyrate dehydrogenase, mitochondrial def: "A protein that is a translation product of the human HIBADH gene or a 1:1 ortholog thereof." [PRO:DNx] comment: Category=gene. synonym: "HIBADH" EXACT PRO-short-label [PRO:DNx] is_a: PR:000000001 ! protein [Term] id: PR:000047694 name: 3-hydroxyisobutyrate dehydrogenase, mitochondrial, transit peptide removed form (human) def: "A 3-hydroxyisobutyrate dehydrogenase, mitochondrial (human) that has had the transit peptide removed. UniProtKB:P31937, 37-336." [PRO:DNx, Reactome:R-HSA-70882] comment: Category=organism-modification. synonym: "PRO_0000007158" EXACT PRO-proteoform-ftid [PRO:DNx] synonym: "hHIBADH/TransPep-" EXACT PRO-short-label [PRO:DNx] synonym: "UniProtKB:P31937, 37-336" EXACT PRO-proteoform-std [PRO:DNx] xref: Reactome:R-HSA-70882 "PR:000047694 located_in GO:0005759" intersection_of: PR:P31937 ! 3-hydroxyisobutyrate dehydrogenase, mitochondrial (human) intersection_of: lacks_part SO:0000725 ! transit_peptide relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:P31937 name: 3-hydroxyisobutyrate dehydrogenase, mitochondrial (human) def: "A 3-hydroxyisobutyrate dehydrogenase, mitochondrial that is encoded in the genome of human." [PRO:DNx, UniProtKB:P31937] comment: Category=organism-gene. synonym: "HIBADH" RELATED Gene-based [UniProtKB:P31937] synonym: "hHIBADH" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:P31937 intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens intersection_of: PR:000008549 ! 3-hydroxyisobutyrate dehydrogenase, mitochondrial relationship: has_gene_template HGNC:4907 ! HIBADH (human)