[Term] id: PR:000047695 name: 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial, transit peptide removed form (human) def: "A 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial (human) that has had the transit peptide removed. UniProtKB:Q6NVY1, 33-386." [PRO:DNx, Reactome:R-HSA-70872] comment: Category=organism-modification. synonym: "PRO_0000284929" EXACT PRO-proteoform-ftid [PRO:DNx] synonym: "hHIBCH/TransPep-" EXACT PRO-short-label [PRO:DNx] synonym: "UniProtKB:Q6NVY1, 33-386" EXACT PRO-proteoform-std [PRO:DNx] xref: Reactome:R-HSA-70872 "PR:000047695 located_in GO:0005759" intersection_of: PR:Q6NVY1 ! 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial (human) intersection_of: lacks_part SO:0000725 ! transit_peptide relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:Q6NVY1-1 name: 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial isoform h1 (human) def: "A 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q6NVY1-1." [PRO:DNx, UniProtKB:Q6NVY1] comment: Category=organism-sequence. synonym: "hHIBCH/iso:h1" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q6NVY1-1 is_a: PR:Q6NVY1 ! 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:Q6NVY1 name: 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial (human) def: "A 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial that is encoded in the genome of human." [PRO:DNx, UniProtKB:Q6NVY1] comment: Category=organism-gene. synonym: "HIBCH" RELATED Gene-based [UniProtKB:Q6NVY1] synonym: "hHIBCH" EXACT PRO-short-label [PRO:DNx] synonym: "HIBYL-CoA-H (human)" EXACT [UniProtKB:Q6NVY1] synonym: "HIB-CoA hydrolase (human)" EXACT [UniProtKB:Q6NVY1] synonym: "3-hydroxyisobutyryl-coenzyme A hydrolase (human)" EXACT [UniProtKB:Q6NVY1] xref: UniProtKB:Q6NVY1 intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens intersection_of: PR:000008550 ! 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial relationship: has_gene_template HGNC:4908 ! HIBCH (human) [Term] id: PR:000008550 name: 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial def: "A protein that is a translation product of the human HIBCH gene or a 1:1 ortholog thereof." [PRO:DNx] comment: Category=gene. synonym: "HIBCH" EXACT PRO-short-label [PRO:DNx] synonym: "HIBYL-CoA-H" EXACT [] synonym: "HIB-CoA hydrolase" EXACT [] synonym: "3-hydroxyisobutyryl-coenzyme A hydrolase" EXACT [] is_a: PR:000000001 ! protein [Term] id: PR:Q6NVY1-2 name: 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial isoform h2 (human) def: "A 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q6NVY1-2." [PRO:DNx, UniProtKB:Q6NVY1] comment: Category=organism-sequence. synonym: "hHIBCH/iso:h2" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q6NVY1-2 is_a: PR:Q6NVY1 ! 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens