[Term] id: PR:Q9UDR5 name: alpha-aminoadipic semialdehyde synthase, mitochondrial (human) def: "An alpha-aminoadipic semialdehyde synthase, mitochondrial that is encoded in the genome of human." [PRO:DNx, UniProtKB:Q9UDR5] comment: Category=organism-gene. synonym: "AASS" RELATED Gene-based [UniProtKB:Q9UDR5] synonym: "hAASS" EXACT PRO-short-label [PRO:DNx] synonym: "LKR/SDH (human)" EXACT [UniProtKB:Q9UDR5] xref: UniProtKB:Q9UDR5 intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens intersection_of: PR:000003532 ! alpha-aminoadipic semialdehyde synthase, mitochondrial relationship: has_gene_template HGNC:17366 ! AASS (human) [Term] id: PR:A2VCW9-1 name: alpha-aminoadipic semialdehyde synthase, mitochondrial isoform 1 (rat) def: "An alpha-aminoadipic semialdehyde synthase, mitochondrial isoform 1 that is encoded in the genome of rat." [PRO:DNx] comment: Category=organism-sequence. synonym: "rAASS/iso:1" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:A2VCW9-1 intersection_of: only_in_taxon NCBITaxon:10116 ! Rattus norvegicus intersection_of: PR:000043851 ! alpha-aminoadipic semialdehyde synthase, mitochondrial isoform 1 [Term] id: PR:A2VCW9 name: alpha-aminoadipic semialdehyde synthase, mitochondrial (rat) def: "An alpha-aminoadipic semialdehyde synthase, mitochondrial that is encoded in the genome of rat." [OMA:A2VCW9, PANTHER:PTHR11133:SF1, PRO:DNx] comment: Category=organism-gene. synonym: "Aass" RELATED Gene-based [UniProtKB:A2VCW9] synonym: "rAASS" EXACT PRO-short-label [PRO:DNx] synonym: "LKR/SDH (rat)" EXACT [UniProtKB:A2VCW9] xref: UniProtKB:A2VCW9 intersection_of: only_in_taxon NCBITaxon:10116 ! Rattus norvegicus intersection_of: PR:000003532 ! alpha-aminoadipic semialdehyde synthase, mitochondrial relationship: has_gene_template RGD:1310811 ! Aass (rat) [Term] id: PR:Q9UDR5-1 name: alpha-aminoadipic semialdehyde synthase, mitochondrial isoform 1 (human) def: "An alpha-aminoadipic semialdehyde synthase, mitochondrial isoform 1 that is encoded in the genome of human." [PRO:DNx] comment: Category=organism-sequence. synonym: "hAASS/iso:1" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q9UDR5-1 intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens intersection_of: PR:000043851 ! alpha-aminoadipic semialdehyde synthase, mitochondrial isoform 1 [Term] id: PR:Q9SMZ4-1 name: alpha-aminoadipic semialdehyde synthase isoform Long (Arabidopsis thaliana) def: "An alpha-aminoadipic semialdehyde synthase (Arabidopsis thaliana) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q9SMZ4-1." [PRO:DNx, UniProtKB:Q9SMZ4] comment: Category=organism-sequence. synonym: "At-AASS/iso:Long" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q9SMZ4-1 is_a: PR:Q9SMZ4 ! alpha-aminoadipic semialdehyde synthase (Arabidopsis thaliana) relationship: only_in_taxon NCBITaxon:3702 ! Arabidopsis thaliana [Term] id: PR:Q99K67 name: alpha-aminoadipic semialdehyde synthase, mitochondrial (mouse) def: "An alpha-aminoadipic semialdehyde synthase, mitochondrial that is encoded in the genome of mouse." [OMA:Q99K67, PRO:DNx] comment: Category=organism-gene. synonym: "Aass" RELATED Gene-based [UniProtKB:Q99K67] synonym: "mAASS" EXACT PRO-short-label [PRO:DNx] synonym: "Lorsdh" RELATED Gene-based [UniProtKB:Q99K67] synonym: "LKR/SDH (mouse)" EXACT [UniProtKB:Q99K67] xref: UniProtKB:Q99K67 intersection_of: only_in_taxon NCBITaxon:10090 ! Mus musculus intersection_of: PR:000003532 ! alpha-aminoadipic semialdehyde synthase, mitochondrial relationship: has_gene_template MGI:1353573 ! Aass (mouse) [Term] id: PR:Q9SMZ4-2 name: alpha-aminoadipic semialdehyde synthase isoform Short (Arabidopsis thaliana) def: "An alpha-aminoadipic semialdehyde synthase (Arabidopsis thaliana) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q9SMZ4-2." [PRO:DNx, UniProtKB:Q9SMZ4] comment: Category=organism-sequence. synonym: "At-AASS/iso:Short" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q9SMZ4-2 is_a: PR:Q9SMZ4 ! alpha-aminoadipic semialdehyde synthase (Arabidopsis thaliana) relationship: only_in_taxon NCBITaxon:3702 ! Arabidopsis thaliana [Term] id: PR:Q9SMZ4 name: alpha-aminoadipic semialdehyde synthase (Arabidopsis thaliana) def: "An alpha-aminoadipic semialdehyde synthase, mitochondrial that is encoded in the genome of Arabidopsis thaliana." [OMA:Q9SMZ4, PRO:DNx] comment: Category=organism-gene. synonym: "LKR" RELATED Gene-based [UniProtKB:Q9SMZ4] synonym: "SDH" RELATED Gene-based [UniProtKB:Q9SMZ4] synonym: "At-AASS" EXACT PRO-short-label [PRO:DNx] synonym: "LKR/SDH" RELATED Gene-based [UniProtKB:Q9SMZ4] synonym: "F4I10.80" RELATED Gene-based [UniProtKB:Q9SMZ4] synonym: "At4g33150" RELATED Gene-based [UniProtKB:Q9SMZ4] synonym: "cAt-LKR/SDH (Arabidopsis thaliana)" EXACT [UniProtKB:Q9SMZ4] xref: UniProtKB:Q9SMZ4 intersection_of: only_in_taxon NCBITaxon:3702 ! Arabidopsis thaliana intersection_of: PR:000003532 ! alpha-aminoadipic semialdehyde synthase, mitochondrial relationship: has_gene_template Araport:AT4G33150 ! LKR/SDH (Arabidopsis thaliana) [Term] id: PR:000018843 name: alpha-aminoadipic semialdehyde synthase, mitochondrial, transit peptide removed form def: "An alpha-aminoadipic semialdehyde synthase, mitochondrial that has had the transit peptide removed." [PRO:DNx] comment: Category=modification. synonym: "AASS/TransPep-" EXACT PRO-short-label [PRO:DNx] intersection_of: PR:000003532 ! alpha-aminoadipic semialdehyde synthase, mitochondrial intersection_of: lacks_part SO:0000725 ! transit_peptide [Term] id: PR:000046215 name: alpha-aminoadipic semialdehyde synthase, mitochondrial, transit peptide removed form (human) def: "An alpha-aminoadipic semialdehyde synthase, mitochondrial (human) that has had the transit peptide removed. UniProtKB:Q9UDR5, 33-926." [PRO:DNx, Reactome:R-HSA-70924] comment: Category=organism-modification. synonym: "PRO_0000001052" EXACT PRO-proteoform-ftid [PRO:DNx] synonym: "hAASS/TransPep-" EXACT PRO-short-label [PRO:DNx] synonym: "UniProtKB:Q9UDR5, 33-926" EXACT PRO-proteoform-std [PRO:DNx] xref: Reactome:R-HSA-70924 "PR:000046215 located_in GO:0005759" intersection_of: PR:Q9UDR5 ! alpha-aminoadipic semialdehyde synthase, mitochondrial (human) intersection_of: lacks_part SO:0000725 ! transit_peptide relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:000003532 name: alpha-aminoadipic semialdehyde synthase, mitochondrial def: "A protein that is a translation product of the human AASS gene or a 1:1 ortholog thereof." [PRO:DNx] comment: Category=gene. synonym: "AASS" EXACT PRO-short-label [PRO:DNx] synonym: "Lorsdh" RELATED Gene-based [] synonym: "LKR/SDH" EXACT [] is_a: PR:000000001 ! protein [Term] id: PR:Q99K67-1 name: alpha-aminoadipic semialdehyde synthase, mitochondrial isoform 1 (mouse) def: "An alpha-aminoadipic semialdehyde synthase, mitochondrial isoform 1 that is encoded in the genome of mouse." [PRO:DNx] comment: Category=organism-sequence. synonym: "mAASS/iso:1" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q99K67-1 intersection_of: only_in_taxon NCBITaxon:10090 ! Mus musculus intersection_of: PR:000043851 ! alpha-aminoadipic semialdehyde synthase, mitochondrial isoform 1 [Term] id: PR:000043851 name: alpha-aminoadipic semialdehyde synthase, mitochondrial isoform 1 def: "An alpha-aminoadipic semialdehyde synthase, mitochondrial that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q9UDR5-1 or a 1:1 ortholog thereof." [PRO:DNx] comment: Category=sequence. synonym: "AASS/iso:1" EXACT PRO-short-label [PRO:DNx] is_a: PR:000003532 ! alpha-aminoadipic semialdehyde synthase, mitochondrial