[Term] id: PR:000044195 name: trifunctional enzyme subunit alpha, mitochondrial, transit peptide removed form (human) def: "A trifunctional enzyme subunit alpha, mitochondrial (human) that has had the transit peptide removed. Example: UniProtKB:P40939-1, 37-763." [PRO:DAN] comment: Category=organism-modification. synonym: "PRO_0000007403" NARROW PRO-proteoform-ftid [PRO:DNx] synonym: "hHADHA/TransPep-" EXACT PRO-short-label [PRO:DAN] synonym: "UniProtKB:P40939-1, 37-763" NARROW PRO-proteoform-std [PRO:DNx] xref: Reactome:R-HSA-77264 "PR:000044195 located_in GO:0005743" intersection_of: PR:P40939 ! trifunctional enzyme subunit alpha, mitochondrial (human) intersection_of: lacks_part SO:0000725 ! transit_peptide relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:P40939-1 name: trifunctional enzyme subunit alpha, mitochondrial isoform 1 (human) def: "A trifunctional enzyme subunit alpha, mitochondrial isoform 1 that is encoded in the genome of human." [PRO:HJD] comment: Category=organism-sequence. synonym: "hHADHA/iso:1" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:P40939-1 intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens intersection_of: PR:000027059 ! trifunctional enzyme subunit alpha, mitochondrial isoform 1 [Term] id: PR:Q8BMS1 name: trifunctional enzyme subunit alpha, mitochondrial (mouse) def: "A trifunctional enzyme subunit alpha, mitochondrial that is encoded in the genome of mouse." [OMA:Q8BMS1, PRO:DNx] comment: Category=organism-gene. synonym: "Hadha" RELATED Gene-based [UniProtKB:Q8BMS1] synonym: "mHADHA" EXACT PRO-short-label [PRO:DNx] synonym: "TP-alpha (mouse)" EXACT [UniProtKB:Q8BMS1] synonym: "monolysocardiolipin acyltransferase (mouse)" EXACT [UniProtKB:Q8BMS1] xref: UniProtKB:Q8BMS1 intersection_of: only_in_taxon NCBITaxon:10090 ! Mus musculus intersection_of: PR:000008433 ! trifunctional enzyme subunit alpha, mitochondrial relationship: has_gene_template MGI:2135593 ! Hadha (mouse) [Term] id: PR:Q64428 name: trifunctional enzyme subunit alpha, mitochondrial (rat) def: "A trifunctional enzyme subunit alpha, mitochondrial that is encoded in the genome of rat." [OMA:Q64428, PMID:8253773, PRO:HJD] comment: Category=organism-gene. synonym: "Hadha" RELATED Gene-based [UniProtKB:Q64428] synonym: "rHADHA" EXACT PRO-short-label [PRO:DNx] synonym: "TP-alpha (rat)" EXACT [UniProtKB:Q64428] synonym: "monolysocardiolipin acyltransferase (rat)" EXACT [UniProtKB:Q64428] xref: UniProtKB:Q64428 intersection_of: only_in_taxon NCBITaxon:10116 ! Rattus norvegicus intersection_of: PR:000008433 ! trifunctional enzyme subunit alpha, mitochondrial relationship: has_gene_template RGD:620512 ! Hadha (rat) [Term] id: PR:P40939-2 name: trifunctional enzyme subunit alpha, mitochondrial isoform h2 (human) def: "A trifunctional enzyme subunit alpha, mitochondrial (human) that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:P40939-2." [PRO:DNx, UniProtKB:P40939] comment: Category=organism-sequence. synonym: "hHADHA/iso:h2" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:P40939-2 is_a: PR:P40939 ! trifunctional enzyme subunit alpha, mitochondrial (human) relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens [Term] id: PR:000027059 name: trifunctional enzyme subunit alpha, mitochondrial isoform 1 def: "A trifunctional enzyme subunit alpha, mitochondrial that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q8BMS1-1 or a 1:1 ortholog thereof." [PMID:16141072, PMID:16916647, PRO:HJD] comment: Category=sequence. synonym: "HADHA/iso:1" EXACT PRO-short-label [PRO:DNx] is_a: PR:000008433 ! trifunctional enzyme subunit alpha, mitochondrial [Term] id: PR:P40939 name: trifunctional enzyme subunit alpha, mitochondrial (human) def: "A trifunctional enzyme subunit alpha, mitochondrial that is encoded in the genome of human." [PRO:DNx] comment: Category=organism-gene. synonym: "HADH" RELATED Gene-based [UniProtKB:P40939] synonym: "HADHA" RELATED Gene-based [UniProtKB:P40939] synonym: "hHADHA" EXACT PRO-short-label [PRO:DNx] synonym: "TP-alpha (human)" EXACT [UniProtKB:P40939] synonym: "78 kDa gastrin-binding protein (human)" EXACT [UniProtKB:P40939] synonym: "monolysocardiolipin acyltransferase (human)" EXACT [UniProtKB:P40939] xref: UniProtKB:P40939 intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens intersection_of: PR:000008433 ! trifunctional enzyme subunit alpha, mitochondrial relationship: has_gene_template HGNC:4801 ! HADHA (human) [Term] id: PR:Q8BMS1-1 name: trifunctional enzyme subunit alpha, mitochondrial isoform 1 (mouse) def: "A trifunctional enzyme subunit alpha, mitochondrial isoform 1 that is encoded in the genome of mouse." [PMID:16141072, PMID:16916647, PRO:HJD] comment: Category=organism-sequence. synonym: "TP-alpha" RELATED [] synonym: "mHADHA/iso:1" EXACT PRO-short-label [PRO:DNx] xref: UniProtKB:Q8BMS1-1 intersection_of: only_in_taxon NCBITaxon:10090 ! Mus musculus intersection_of: PR:000027059 ! trifunctional enzyme subunit alpha, mitochondrial isoform 1 [Term] id: PR:000008433 name: trifunctional enzyme subunit alpha, mitochondrial def: "A protein that is a translation product of the human HADHA gene or a 1:1 ortholog thereof." [PRO:DNx] comment: Category=gene. synonym: "HADH" RELATED Gene-based [] synonym: "HADHA" EXACT PRO-short-label [PRO:DNx] synonym: "TP-alpha" EXACT [] synonym: "78 kDa gastrin-binding protein" EXACT [] synonym: "monolysocardiolipin acyltransferase" EXACT [] is_a: PR:000000001 ! protein