[Term] id: PR:P21953 name: 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human) def: "A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial that is encoded in the genome of human." [PRO:DNx, UniProtKB:P21953] comment: Category=organism-gene. synonym: "BCKDHB" RELATED Gene-based [UniProtKB:P21953] synonym: "hBCKDHB" EXACT PRO-short-label [PRO:DNx] synonym: "BCKDE1B (human)" EXACT [UniProtKB:P21953] synonym: "BCKDH E1-beta (human)" EXACT [UniProtKB:P21953] synonym: "branched-chain alpha-keto acid dehydrogenase E1 component beta chain (human)" EXACT [UniProtKB:P21953] xref: UniProtKB:P21953 intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens intersection_of: PR:000004687 ! 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial relationship: has_gene_template HGNC:987 ! BCKDHB (human)