[Term] id: PR:000027059 name: trifunctional enzyme subunit alpha, mitochondrial isoform 1 def: "A trifunctional enzyme subunit alpha, mitochondrial that is a translation product of some mRNA whose exon structure and start site selection renders it capable of giving rise to a protein with the amino acid sequence represented by UniProtKB:Q8BMS1-1 or a 1:1 ortholog thereof." [PRO:HJD, PMID:16141072, PMID:16916647] comment: Category=sequence. synonym: "HADHA/iso:1" EXACT PRO-short-label [PRO:DNx] property_value: has_archetype PR:Q8BMS1-1 is_a: PR:000008433 ! trifunctional enzyme subunit alpha, mitochondrial