[Term] id: PR:P00480 name: ornithine transcarbamylase, mitochondrial (human) def: "An ornithine transcarbamylase, mitochondrial that is encoded in the genome of human." [PRO:DNx, UniProtKB:P00480] comment: Category=organism-gene. synonym: "hOTC" EXACT PRO-short-label [PRO:DNx] synonym: "ornithine carbamoyltransferase, mitochondrial (human)" EXACT [UniProtKB:P00480] synonym: "OTCase (human)" EXACT [UniProtKB:P00480] synonym: "OTC" RELATED Gene-based [UniProtKB:P00480] xref: UniProtKB:P00480 xref: Reactome:R-HSA-8986136 "PR:P00480 located_in GO:0005758" xref: Reactome:R-HSA-8986146 "PR:P00480 located_in GO:0005743" intersection_of: PR:000012070 ! ornithine transcarbamylase, mitochondrial intersection_of: only_in_taxon NCBITaxon:9606 ! Homo sapiens relationship: has_gene_template HGNC:8512 ! OTC (human) relationship: has_canonical_sequence UniProtKB:P00480 ! P00480-1