[Term]
id: PR:000048350
name: methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial, transit peptide removed biotinylated 1 (human)
def: "A methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial (human) that has had the transit peptide removed and has been post-translationally modified to include biotinylated lysine at position 681 of the amino acid sequence represented by UniProtKB:Q96RQ3. UniProtKB:Q96RQ3, 42-725, Lys-681, MOD:00126." [PRO:DNx, Reactome:R-HSA-3323154, Reactome:R-HSA-70748]
comment: Category=organism-modification.
synonym: "hMCCC1/TransPep-/Btn:1" EXACT PRO-short-label [PRO:DNx]
synonym: "PRO_0000002833, Lys-681, MOD:00126" EXACT PRO-proteoform-ftid [PRO:DNx]
synonym: "UniProtKB:Q96RQ3, 42-725, Lys-681, MOD:00126" EXACT PRO-proteoform-std [PRO:DNx]
xref: Reactome:R-HSA-3323154 "PR:000048350 located_in GO:0005829"
xref: Reactome:R-HSA-70748 "PR:000048350 located_in GO:0005759"
is_a: PR:Q96RQ3 ! methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial (human)
relationship: has_part MOD:00126 ! N6-biotinyl-L-lysine
relationship: lacks_part SO:0000725 ! transit_peptide
relationship: only_in_taxon NCBITaxon:9606 ! Homo sapiens