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Reset to default PRO Hierarchy Protein Ontology Hierarchy (Note that the implicit relationship is is_a, whereas derives from indicates derives_from relationship.)
  25 shown from total 255930 nodes






Category
PR:000018263  amino acid chain
 polymer
PR:000000001  protein
 
PR:000004686  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
 gene
PR:P12694  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial (human)
 organism-gene
PR:P12694-1  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform h1 (human)
 organism-sequence
PR:P12694-2  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform h2 (human)
 organism-sequence
PR:000046471  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial, transit peptide removed form (human)
 organism-modification
PR:000085929  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant A285P, transit peptide removed form (human)
 organism-modification
PR:000085940  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant G249S, transit peptide removed form (human)
 organism-modification
PR:000085894  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant G290N, transit peptide removed form (human)
 organism-modification
PR:000085806  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant T310R, transit peptide removed form (human)
 organism-modification
PR:000085873  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant Y413C, transit peptide removed form (human)
 organism-modification
PR:000085912  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant Y438N, transit peptide removed form (human)
 organism-modification
PR:000036194  eukaryotic protein
 
PR:000029067  Homo sapiens protein
 
PR:P12694  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial (human)
 organism-gene
PR:P12694-1  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform h1 (human)
 organism-sequence
PR:P12694-2  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform h2 (human)
 organism-sequence
PR:000046471  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial, transit peptide removed form (human)
 organism-modification
PR:000085929  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant A285P, transit peptide removed form (human)
 organism-modification
PR:000085940  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant G249S, transit peptide removed form (human)
 organism-modification
PR:000085894  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant G290N, transit peptide removed form (human)
 organism-modification
PR:000085806  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant T310R, transit peptide removed form (human)
 organism-modification
PR:000085873  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant Y413C, transit peptide removed form (human)
 organism-modification
PR:000085912  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant Y438N, transit peptide removed form (human)
 organism-modification