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Protein Ontology report - 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human)
PR:P21953 - http://purl.obolibrary.org/obo/PR_P21953
 
  Protein Forms      
Ontology Information Show OBO stanza
  PRO ID
PR:P21953   
  PRO name2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human) 
  Synonyms
PRO-Short-label: EXACT:hBCKDHB
Gene-based: RELATED:BCKDHB
Other: EXACT:BCKDE1B (human) | BCKDH E1-beta (human) | branched-chain alpha-keto acid dehydrogenase E1 component beta chain (human)
  Definition"A 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial that is encoded in the genome of human." [PRO:DNx, UniProtKB:P21953
  PRO Categoryorganism-gene 
  ParentPR:000004687 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
PR:000029067 Homo sapiens protein
  Gene TemplateHGNC:987 BCKDHB (human)
  TaxonNCBITaxon:9606 Homo sapiens
  Terms by PRO Category
Organism-Independent Organism-Specific
         Category          Number of Terms          Category          Number of Terms
         Gene0                                                  Organism-Gene 1                                        
         Sequence0                                                  Organism-Sequence 2                                        
         Modification0                                                  Organism-Modification 10                                        
  Term Hierarchy
  Visualization
DAG: OLS:
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Related Cross References

  Db identifiers
UniProtKB:P21953
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Protein Forms  Switch to Extended View   

Category  

PRO Form Name

Short Name

Ann. Has Annotation?

Comp. In Complex?
organism-gene



PR:P21953 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (human)

hBCKDHB


organism-sequence



PR:P21953-1 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform h1 (human)

hBCKDHB/iso:h1


organism-sequence



PR:P21953-2 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform h2 (human)

hBCKDHB/iso:h2


organism-modification



PR:000046472 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial, transit peptide removed form (human)

hBCKDHB/TransPep-


organism-modification



PR:000062476 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial, transit peptide removed phosphorylated 1 (human)

hBCKDHB/TransPep-/Phos:1


organism-modification



PR:000085816 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial sequence variant G278S, transit peptide removed form (human)

hBCKDHB/var:G278S/TransPep-


organism-modification



PR:000085865 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial sequence variant Q346R, transit peptide removed form (human)

hBCKDHB/var:Q346R/TransPep-


organism-modification



PR:000085904 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial sequence variant N176Y, transit peptide removed form (human)

hBCKDHB/var:N176Y/TransPep-


organism-modification



PR:000085906 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial sequence variant R170H, transit peptide removed form (human)

hBCKDHB/var:R170H/TransPep-


organism-modification



PR:000085988 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial sequence variant R183P, transit peptide removed form (human)

hBCKDHB/var:R183P/TransPep-


organism-modification



PR:000086004 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial sequence variant H206R, transit peptide removed form (human)

hBCKDHB/var:H206R/TransPep-


organism-modification



PR:000071288 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial methylated 1 (human)

hBCKDHB/Me:1


organism-modification



PR:000079222 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial methylated 2 (human)

hBCKDHB/Me:2