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gene
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   PR:000004686 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial |   BCKDHA |

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organism-gene
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   PR:O45924 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial (worm) |   BCKDHA (worm) |

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organism-gene
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   PR:P12694 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial (human) |   hBCKDHA |

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organism-sequence
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   PR:P12694-1 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform h1 (human) |   hBCKDHA/iso:h1 |

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organism-sequence
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   PR:P12694-2 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform h2 (human) |   hBCKDHA/iso:h2 |

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organism-modification
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   PR:000046471 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial, transit peptide removed form (human) |   hBCKDHA/TransPep- |

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organism-modification
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   PR:000085806 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant T310R, transit peptide removed form (human) |   hBCKDHA/var:T310R/TransPep- |

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organism-modification
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   PR:000085873 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant Y413C, transit peptide removed form (human) |   hBCKDHA/var:Y413C/TransPep- |

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organism-modification
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   PR:000085894 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant G290N, transit peptide removed form (human) |   hBCKDHA/var:G290N/TransPep- |

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organism-modification
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   PR:000085912 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant Y438N, transit peptide removed form (human) |   hBCKDHA/var:Y438N/TransPep- |

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organism-modification
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   PR:000085929 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant A285P, transit peptide removed form (human) |   hBCKDHA/var:A285P/TransPep- |

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organism-modification
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   PR:000085940 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant G249S, transit peptide removed form (human) |   hBCKDHA/var:G249S/TransPep- |

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modification
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   PR:000019127 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial, transit peptide removed form |   BCKDHA/TransPep- |

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organism-modification
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   PR:000046471 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial, transit peptide removed form (human) |   hBCKDHA/TransPep- |

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organism-modification
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   PR:000085806 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant T310R, transit peptide removed form (human) |   hBCKDHA/var:T310R/TransPep- |

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organism-modification
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   PR:000085873 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant Y413C, transit peptide removed form (human) |   hBCKDHA/var:Y413C/TransPep- |

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organism-modification
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   PR:000085894 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant G290N, transit peptide removed form (human) |   hBCKDHA/var:G290N/TransPep- |

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organism-modification
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   PR:000085912 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant Y438N, transit peptide removed form (human) |   hBCKDHA/var:Y438N/TransPep- |

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organism-modification
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   PR:000085929 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant A285P, transit peptide removed form (human) |   hBCKDHA/var:A285P/TransPep- |

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organism-modification
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   PR:000085940 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant G249S, transit peptide removed form (human) |   hBCKDHA/var:G249S/TransPep- |

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