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Protein Ontology report - 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
PR:000004686 - http://purl.obolibrary.org/obo/PR_000004686
 
  Protein Forms      
Ontology Information Show OBO stanza
  PRO ID
PR:000004686   
  PRO name2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial 
  Synonyms
PRO-Short-label: EXACT:BCKDHA
Other: EXACT:BCKDE1A | BCKDH E1-alpha | branched-chain alpha-keto acid dehydrogenase E1 component alpha chain
  Definition"A protein that is a translation product of the human BCKDHA gene or a 1:1 ortholog thereof." [PRO:DNx] 
  PRO Categorygene 
  ParentPR:000000001 protein
  Terms by PRO Category
Organism-Independent Organism-Specific
         Category          Number of Terms          Category          Number of Terms
         Gene1                                                  Organism-Gene 2                                        
         Sequence0                                                  Organism-Sequence 2                                        
         Modification1                                                  Organism-Modification 7                                        
  Term Hierarchy
  Visualization
DAG: OLS:
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Protein Forms  Switch to Extended View   

Category  

PRO Form Name

Short Name

Ann. Has Annotation?

Comp. In Complex?
gene



PR:000004686 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial

BCKDHA


organism-gene



PR:O45924 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial (worm)

BCKDHA (worm)


organism-gene



PR:P12694 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial (human)

hBCKDHA


organism-sequence



PR:P12694-1 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform h1 (human)

hBCKDHA/iso:h1


organism-sequence



PR:P12694-2 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform h2 (human)

hBCKDHA/iso:h2


organism-modification



PR:000046471 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial, transit peptide removed form (human)

hBCKDHA/TransPep-


organism-modification



PR:000085806 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant T310R, transit peptide removed form (human)

hBCKDHA/var:T310R/TransPep-


organism-modification



PR:000085873 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant Y413C, transit peptide removed form (human)

hBCKDHA/var:Y413C/TransPep-


organism-modification



PR:000085894 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant G290N, transit peptide removed form (human)

hBCKDHA/var:G290N/TransPep-


organism-modification



PR:000085912 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant Y438N, transit peptide removed form (human)

hBCKDHA/var:Y438N/TransPep-


organism-modification



PR:000085929 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant A285P, transit peptide removed form (human)

hBCKDHA/var:A285P/TransPep-


organism-modification



PR:000085940 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant G249S, transit peptide removed form (human)

hBCKDHA/var:G249S/TransPep-


modification



PR:000019127 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial, transit peptide removed form

BCKDHA/TransPep-


organism-modification



PR:000046471 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial, transit peptide removed form (human)

hBCKDHA/TransPep-


organism-modification



PR:000085806 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant T310R, transit peptide removed form (human)

hBCKDHA/var:T310R/TransPep-


organism-modification



PR:000085873 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant Y413C, transit peptide removed form (human)

hBCKDHA/var:Y413C/TransPep-


organism-modification



PR:000085894 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant G290N, transit peptide removed form (human)

hBCKDHA/var:G290N/TransPep-


organism-modification



PR:000085912 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant Y438N, transit peptide removed form (human)

hBCKDHA/var:Y438N/TransPep-


organism-modification



PR:000085929 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant A285P, transit peptide removed form (human)

hBCKDHA/var:A285P/TransPep-


organism-modification



PR:000085940 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial sequence variant G249S, transit peptide removed form (human)

hBCKDHA/var:G249S/TransPep-